{"id":171581,"date":"2019-06-20T10:46:55","date_gmt":"2019-06-20T07:46:55","guid":{"rendered":"http:\/\/www.tvturk.com\/index.php\/als-hastaligi-erkeklerde-daha-cok-goruluyor\/"},"modified":"2019-06-20T10:46:55","modified_gmt":"2019-06-20T07:46:55","slug":"als-hastaligi-erkeklerde-daha-cok-goruluyor","status":"publish","type":"post","link":"http:\/\/www.tvturk.com\/index.php\/als-hastaligi-erkeklerde-daha-cok-goruluyor\/","title":{"rendered":"ALS hastal\u0131\u011f\u0131 erkeklerde daha \u00e7ok g\u00f6r\u00fcl\u00fcyor"},"content":{"rendered":"<p>N\u00f6roloji Uzman\u0131 Do\u00e7. Dr. Sibel Karaca, \u00e7\u0131k\u0131\u015f sebebi hen\u00fcz bilinmeyen ALS\u2019nin 40 ila 50 ya\u015f aras\u0131ndaki erkekleri daha \u00e7ok etkiledi\u011fini belirterek, \u201cALS\u2019nin hen\u00fcz kesin tedavisi bulunmad\u0131\u011f\u0131ndan hastan\u0131n bu s\u00fcre\u00e7te m\u00fcmk\u00fcn oldu\u011funca rahat ettirilmesi ve normal ya\u015fam\u0131n\u0131 s\u00fcrd\u00fcrmesini sa\u011flayacak tedbirlerin al\u0131nmas\u0131 \u00f6nemli\u201d dedi.<\/p>\n<p>Sinsi ve yava\u015f bir seyir g\u00f6stermesinden dolay\u0131 \u00e7o\u011fu kez ilk etapta fark\u0131na bile var\u0131lamayan bir hastal\u0131k t\u00fcr\u00fc olan ALS, ilerleyici bir sinir sistemi hastal\u0131\u011f\u0131 oldu\u011fundan zamanla motor sinirleri etkileyerek kas hareketlerine engel oluyor, hastal\u0131\u011f\u0131n ileri evrelerinde ise fel\u00e7 geli\u015fiyor. Hastal\u0131\u011f\u0131n ortaya \u00e7\u0131k\u0131\u015f sebebinin hen\u00fcz tam olarak bilinmedi\u011fini ve kesin tedavisinin olmad\u0131\u011f\u0131n\u0131 s\u00f6yleyen Medline Adana Hastanesi N\u00f6roloji Uzman\u0131 Do\u00e7. Dr. Sibel Karaca, ALS\u2019nin 40 ila 50 ya\u015f aras\u0131ndaki erkekleri nispeten daha \u00e7ok etkiledi\u011fini belirtti.<\/p>\n<p>Sinir sistemini etkiliyor<\/p>\n<p>Kaslar\u0131n ihtiyaca g\u00f6re kas\u0131labilmesi i\u00e7in \u2018motor sinirler\u2019 denen bir grup sinirin g\u00f6rev yapt\u0131\u011f\u0131n\u0131 ifade eden Do\u00e7. Dr. Karaca, \u201cE\u011fer motor sinirlerde tahribat olursa istemli kas kas\u0131lmas\u0131 bozulur. Hasta da g\u00fcc\u00fcn\u00fc k\u0131smen veya tamamen kaybeder. Ancak ALS, v\u00fccudun b\u00fct\u00fcn kaslar\u0131n\u0131 etkilemez. Hasta, ba\u011f\u0131rsaklar\u0131n\u0131 ve idrar\u0131n\u0131 kontrol edebilir. Kalp kas\u0131 zarar g\u00f6rmez, cinsel fonksiyonlar\u0131 etkilenmez. G\u00f6z kaslar\u0131 ise \u00e7o\u011fu kez en son etkilenen kas olur, kimi zaman da hi\u00e7 etkilenmez\u201d dedi.<\/p>\n<p>Ba\u015fka hastal\u0131klarla kar\u0131\u015ft\u0131r\u0131labiliyor<\/p>\n<p>Hastal\u0131\u011f\u0131n te\u015fhisinin klinik belirti ve bulgulara dayanarak kondu\u011funu s\u00f6yleyen Do\u00e7. Dr. Karaca, \u201cYine de ALS pek \u00e7ok kas ve sinir hastal\u0131\u011f\u0131 ile kar\u0131\u015ft\u0131r\u0131labildi\u011fi i\u00e7in baz\u0131 tetkiklerin yap\u0131lmas\u0131 gerekir. En \u00f6nemli tan\u0131sal test EMG\u2019dir. Manyetik rezonans g\u00f6r\u00fcnt\u00fcleme (MR), baz\u0131 kan, idrar ve beyin omurilik suyu tetkiklerinin de duruma g\u00f6re gerekebiliyor\u201d diye konu\u015ftu.<\/p>\n<p>Daha \u00e7ok 40-50 ya\u015f aras\u0131n\u0131 etkiliyor<\/p>\n<p>ALS hastalar\u0131n\u0131n y\u00fczde 90\u2019\u0131n\u0131n rastlant\u0131sal, y\u00fczde 10\u2019unun ise ailesel ALS hastas\u0131 olduklar\u0131n\u0131 kaydeden Do\u00e7. Dr. Karaca, \u201cBu nedenle hastal\u0131\u011f\u0131n b\u00fcy\u00fck oranda kal\u0131t\u0131mla ilgisiz oldu\u011fu s\u00f6ylenebilir. D\u00fcnya geneline bakt\u0131\u011f\u0131m\u0131zda her 100 bin ki\u015filik toplumun 8 ila 10 bireyinde ALS hastal\u0131\u011f\u0131 oldu\u011funu g\u00f6r\u00fcyoruz. Hemen her ya\u015f grubunda rastlansa da daha \u00e7ok 40 ila 50 ya\u015f civar\u0131nda g\u00f6r\u00fcl\u00fcr ve erkekler kad\u0131nlara g\u00f6re daha s\u0131k yakalan\u0131rlar. ALS\u2019ye \u00e7ocuklar aras\u0131nda rastlanma oran\u0131 ise olduk\u00e7a d\u00fc\u015f\u00fckt\u00fcr ve bula\u015f\u0131c\u0131 de\u011fildir\u201d ifadelerini kulland\u0131.<\/p>\n<p>Hasta hareket kabiliyetini yitiriyor<\/p>\n<p>ALS\u2019nin zaman i\u00e7inde ba\u015flad\u0131\u011f\u0131 b\u00f6l\u00fcmden di\u011fer uzuvlara da yay\u0131ld\u0131\u011f\u0131n\u0131 kaydeden Do\u00e7. Dr. Karaca, t\u00fcm kaslarda erime, g\u00fc\u00e7s\u00fczl\u00fck ve se\u011firmeler nedeniyle hastan\u0131n g\u00fcnl\u00fck ya\u015fam aktivitesini k\u0131s\u0131tlayabildi\u011fini belirterek, \u201c\u0130lerlemenin artt\u0131\u011f\u0131 durumlarda hasta yemek yiyemez, giyinemez, y\u0131kanamaz hatta yataktan dahi kalkamaz hale geliyor. Hastal\u0131\u011f\u0131n kritik d\u00f6nemi ise solunum kaslar\u0131n\u0131n da g\u00fc\u00e7s\u00fczle\u015fti\u011fi s\u00fcre\u00e7 oluyor. Solunum ve beslenme yetersizli\u011fi ortaya \u00e7\u0131kt\u0131\u011f\u0131nda hastan\u0131n h\u0131zl\u0131 ve yak\u0131n t\u0131bbi deste\u011fe ihtiyac\u0131 oluyor. Bu durumdaki hastalara ta\u015f\u0131nabilir solunum makinesi ve beslenme amac\u0131yla mideden hortum tak\u0131lmas\u0131 gerekebiliyor\u201d dedi.<\/p>\n<p>Tedavisi hen\u00fcz yok<\/p>\n<p>Hastal\u0131\u011f\u0131n sigara i\u00e7enlerle i\u015f yerinde kur\u015fun gibi metal ve \u00e7e\u015fitli kimyasallara maruz kalan ki\u015filerde ortaya \u00e7\u0131kma riskinin daha y\u00fcksek oldu\u011funun d\u00fc\u015f\u00fcn\u00fcld\u00fc\u011f\u00fcn\u00fc s\u00f6yleyen Do\u00e7. Dr. Karaca, \u201cALS\u2019nin hen\u00fcz kesin tedavisi bulunmad\u0131\u011f\u0131ndan hastan\u0131n bu s\u00fcre\u00e7te m\u00fcmk\u00fcn oldu\u011funca rahat ettirilmesi ve normal ya\u015fam\u0131n\u0131 s\u00fcrd\u00fcrmesini sa\u011flayacak tedbirlerin al\u0131nmas\u0131 \u00f6nemli. G\u00fcn\u00fcm\u00fczde bu hastalar\u0131n rehabilitasyonuna y\u00f6nelik pek \u00e7ok imkan var. Belirtileri kontrol alt\u0131na almak ve yava\u015flatmak i\u00e7in \u00e7e\u015fitli ila\u00e7 tedavileri, fizik tedavi y\u00f6ntemleri mevcut\u201d diye konu\u015ftu.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>N\u00d6ROLOJ\u0130 UZMANI DO\u00c7. DR. S\u0130BEL KARACA, \u00c7IKI\u015e SEBEB\u0130 HEN\u00dcZ B\u0130L\u0130NMEYEN ALS\u2019N\u0130N 40 \u0130LA 50 YA\u015e ARASINDAK\u0130 ERKEKLER\u0130 DAHA \u00c7OK ETK\u0130LED\u0130\u011e\u0130N\u0130 BEL\u0130RTEREK, \u201cALS\u2019N\u0130N HEN\u00dcZ KES\u0130N TEDAV\u0130S\u0130 BULUNMADI\u011eINDAN HASTANIN BU S\u00dcRE\u00c7TE M\u00dcMK\u00dcN OLDU\u011eUNCA RAHAT ETT\u0130R\u0130LMES\u0130 VE NORMAL YA\u015eAMINI S\u00dcRD\u00dcRMES\u0130N\u0130 SA\u011eLAYACAK TEDB\u0130RLER\u0130N ALINMASI \u00d6NEML\u0130\u201d DED\u0130.<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_jetpack_newsletter_access":"","_jetpack_dont_email_post_to_subs":false,"_jetpack_newsletter_tier_id":0,"_jetpack_memberships_contains_paywalled_content":false,"_jetpack_memberships_contains_paid_content":false,"footnotes":"","jetpack_publicize_message":"","jetpack_publicize_feature_enabled":true,"jetpack_social_post_already_shared":true,"jetpack_social_options":{"image_generator_settings":{"template":"highway","default_image_id":0,"font":"","enabled":false},"version":2},"jetpack_post_was_ever_published":false},"categories":[1],"tags":[19415,105,1018,2842,3849,13970],"class_list":["post-171581","post","type-post","status-publish","format-standard","hentry","category-genel","tag-als","tag-cok","tag-daha","tag-erkeklerde","tag-goruluyor","tag-hastaligi"],"jetpack_publicize_connections":[],"jetpack_featured_media_url":"","jetpack_sharing_enabled":true,"jetpack_shortlink":"https:\/\/wp.me\/paKIfm-IDr","_links":{"self":[{"href":"http:\/\/www.tvturk.com\/index.php\/wp-json\/wp\/v2\/posts\/171581","targetHints":{"allow":["GET"]}}],"collection":[{"href":"http:\/\/www.tvturk.com\/index.php\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"http:\/\/www.tvturk.com\/index.php\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"http:\/\/www.tvturk.com\/index.php\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"http:\/\/www.tvturk.com\/index.php\/wp-json\/wp\/v2\/comments?post=171581"}],"version-history":[{"count":0,"href":"http:\/\/www.tvturk.com\/index.php\/wp-json\/wp\/v2\/posts\/171581\/revisions"}],"wp:attachment":[{"href":"http:\/\/www.tvturk.com\/index.php\/wp-json\/wp\/v2\/media?parent=171581"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"http:\/\/www.tvturk.com\/index.php\/wp-json\/wp\/v2\/categories?post=171581"},{"taxonomy":"post_tag","embeddable":true,"href":"http:\/\/www.tvturk.com\/index.php\/wp-json\/wp\/v2\/tags?post=171581"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}